Isolated Recurrent Pleuritis Revealing Familial Mediterranean Fever in Adulthood
نویسندگان
چکیده
منابع مشابه
Isolated recurrent pleuritis revealing familial mediterranean Fever in adulthood.
Familial Mediterranean fever (FMF) is a genetic autoinflammatory disease especially affecting populations of Mediterranean origin with an autosomal recessive inheritance. The cardinal manifestations consist of short febrile and painful attacks of peritonitis, arthritis and pleuritis developing during childhood. We report the case of a 26-year-old man of Tunisian descent who had febrile episodes...
متن کاملPatient with Recurrent Polyserositis (Familial Mediterranean Fever).
Familial Mediterranean fever (FMF) is a hereditary autosomal recessive ,systemic, auto-inflammatory disorder characterized by sporadic, unpredictable attacks of fever and serosal inflammation. FMF is caused by mutations in MEFV, a gene located on the short arm of chromosome 16 (16p13) which encodes a protein 'Pyrin'. The disorder has been given various names including familial paroxysmal polyse...
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familial mediterranean fever (fmf) is a relatively rare disorder, characterized by recurrent self-limited attacks of fever and polyserositis. diagnosis is made by clinical features, gene identification on chromosome 16 and clinical response to specific treatment. different types of vasculitis have been reported in fmf. henoch-schönlein purpura (hsp) is one of them, usually with a benign clinica...
متن کاملBone Mineral Density in Egyptian Children with Familial Mediterranean Fever
Background: Familial Mediterranean fever (FMF) has episodic or subclinical inflammation that may lead to a decrease in bone mineral density (BMD). The objective of this study was to assess BMD in Egyptian children with FMF on genetic basis.Methods: A cross sectional study included 45 FMF patients and 25 control children of both sexes in the age range between 3-16 years old. The patients were re...
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Background: Familial Mediterranean fever (FMF) is an autosomal recessive genetic disorder characterized by recurrent episodes of self-limited fever and serosal tissues inflammation. Methods: To evaluate clinical symptoms and common genetic mutations in southwestern Iranian patients with FMF, 20 unrelated patients were enrolled in this study based on clinical criteria. A panel of 12 common ME...
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ژورنال
عنوان ژورنال: Respiration
سال: 2010
ISSN: 1423-0356,0025-7931
DOI: 10.1159/000315474